Dedifferentiated liposarcoma (DDL) is a rare malignant mesenchymal tumor affecting predominantly the retroperitoneum. Complete surgical excision following early diagnosis is crucial in these patients due to a high rate of local recurrence and metastasis. We report a rare case of synchronous retroperitoneal and mesenteric DDL presenting both a diagnostic and therapeutic challenge.
Synchronous retroperitoneal and mesenteric dedifferentiated liposarcoma: case report of a challenging rare disease and literature review
Paolo Di Mattia;Giorgio Maria Paolo Graziano;
2026-01-01
Abstract
Dedifferentiated liposarcoma (DDL) is a rare malignant mesenchymal tumor affecting predominantly the retroperitoneum. Complete surgical excision following early diagnosis is crucial in these patients due to a high rate of local recurrence and metastasis. We report a rare case of synchronous retroperitoneal and mesenteric DDL presenting both a diagnostic and therapeutic challenge.File in questo prodotto:
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